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Early therapy with bosentan may reverse pulmonary vasculopathy in scleroderma patients

G Kovacs, X Kqiku, R Maier, E Aberer, M Brodmann, W Graninger, S Scheidl, N Tröster, H Olschewski · Pneumologie · Ausgabe 03/2010

DOI 10.1055/s-0030-1251115

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Autor:innenG Kovacs, X Kqiku, R Maier, E Aberer, M Brodmann, W Graninger, S Scheidl, N Tröster, H Olschewski
ZeitschriftPneumologie
Ausgabe03/2010
Jahrgang / SeitenNicht angegeben

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Abstract-Vorschau

Aims: Out-of-proportion pulmonary arterial pressure (PAP) increase during exercise may represent an intermediate stage between normal pulmonary hemodynamics and manifest PAH and might precede PAH in systemic sclerosis (SSc). We hypothesised that bosentan treatment might reverse a trend towards progressive pulmonary vasculopathy in such patients. Patients and methods: SSc patients with a resting PAP30mmHg during exer…

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Zitierempfehlung

G Kovacs, X Kqiku, R Maier, E Aberer, M Brodmann, W Graninger, S Scheidl, N Tröster, H Olschewski (2010) Early therapy with bosentan may reverse pulmonary vasculopathy in scleroderma patients. Pneumologie (03). https://doi.org/10.1055/s-0030-1251115

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