CareLit · DOI-Nachweis · Pneumologie
Why do some adults with PiMZ alpha1-antitrypin develop bronchiectasis?
DOI 10.1055/s-0036-1592257
Bibliografische Angaben
Nachweis in CareLit
Autor:innenN Aggarwal, B Martinez Delgado Delgado, S Salipalli, N Matamala, J Rademacher, N Schwerk, T Welte, S Janciauskiene, FC Ringshausen
ZeitschriftPneumologie
Ausgabe10/2016
Jahrgang / SeitenNicht angegeben
Kernaussage aus der Literatur
Abstract-Vorschau
Several reports indicate an association among inherited alpha-1-antitrypsin deficiency (A1ATD), pulmonary infections and bronchiectasis. Most reported A1ATD cases with bronchiectasis are elderly homozygous PiZZ (Glu342Lys) smokers with emphysema. Whether there is an increased risk of pulmonary diseases, including bronchiectasis, in heterozygous PiMZ A1ATD carriers is debated. We describe an 18-year old, non-smoking…
Zitieren
Zitierempfehlung
N Aggarwal, B Martinez Delgado Delgado, S Salipalli, N Matamala, J Rademacher, N Schwerk, T Welte, S Janciauskiene, FC Ringshausen (2016) Why do some adults with PiMZ alpha1-antitrypin develop bronchiectasis?. Pneumologie (10). https://doi.org/10.1055/s-0036-1592257
Mit CareLit weiterarbeiten