CareLit · DOI-Nachweis · Pneumologie
Hyper IgE Syndrome: a rare cause of bronchiectasis
DOI 10.1055/s-0036-1592283
Bibliografische Angaben
Nachweis in CareLit
Autor:innenM Kaponi, S Chrysikos, G Drivas, K Deskata, K Marosis, K Dimakou
ZeitschriftPneumologie
Ausgabe10/2016
Jahrgang / SeitenNicht angegeben
Kernaussage aus der Literatur
Abstract-Vorschau
Introduction: Job's syndrome (Hyper IgE Syndrome – HIES) is a primary immunodeficiency characterized by raised levels of IgE, eczema and recurrent skin and lung infections in childhood, affecting fewer than 1 per million patients. Although defect in STAT3 protein plays a role, diagnosis is based on clinical and laboratory features. Therapy includes antibiotics, with Staph. Aureus being the most common pathogen. Pneu…
Zitieren
Zitierempfehlung
M Kaponi, S Chrysikos, G Drivas, K Deskata, K Marosis, K Dimakou (2016) Hyper IgE Syndrome: a rare cause of bronchiectasis. Pneumologie (10). https://doi.org/10.1055/s-0036-1592283
Mit CareLit weiterarbeiten