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Electrophysiological study in juvenile asymmetric segmental spinal muscular atrophy (Hirayama disease)

W Dietrich, F Erbguth, G Berger, R Gerlach, I Bär, B Schmid · Klinische Neurophysiologie · Ausgabe 04/2008

DOI 10.1055/s-2008-1072855

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Autor:innenW Dietrich, F Erbguth, G Berger, R Gerlach, I Bär, B Schmid
ZeitschriftKlinische Neurophysiologie
Ausgabe04/2008
Jahrgang / SeitenNicht angegeben

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Abstract-Vorschau

Hirayama disease (HD) is characterized by slowly progressive distal amyotrophy of upper limb, usually monolateral, occurring predominantly in young Asian men. The aetiology of HD is not well understood, various aetiologic factors have been suggested such as microcirculatory disturbances of spinal cord or transient cord compression during neck flexion as well as autoimmune, atopic, and genetic factors. We report on a…

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Zitierempfehlung

W Dietrich, F Erbguth, G Berger, R Gerlach, I Bär, B Schmid (2008) Electrophysiological study in juvenile asymmetric segmental spinal muscular atrophy (Hirayama disease). Klinische Neurophysiologie (04). https://doi.org/10.1055/s-2008-1072855

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