CareLit Fachartikel

Pediatric treatment strategies of Pityriasis lichenoides et varioliformis acuta Mucha Habermann–effects and side effects

PP Wolf, M Sticherling, CJ Voskens, M Schroth · Klinische Pädiatrie · 2011 · Heft 03

Dokument
1016396
CareLit-ID
Jahr
2011
Publikation
PDF
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Metadaten
DOI
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Bibliografische Angaben

Zeitschrift
Klinische Pädiatrie
Autor:innen
PP Wolf, M Sticherling, CJ Voskens, M Schroth
Ausgabe
Heft 03 / 2011
Seiten
–
Erschienen: 2011-03-23 00:00:00
ISSN
0300-8630

Zusammenfassung

Aims: Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta Mucha Habermann is a potentially lethal autoimmune disorder characterized by polymorphous generalized skin lesions that rapidely deteriorate associated with a severe disease pattern. Case report: We report on a 22 months old boy, to our knowledge the youngest out of 42 cases reviewed in the literature since its first description in 1966. He presented with bug-bite-like lesions that rapidely progressed into erythematous ulcers with hemorrhagic crusts and necroses including most of the integument. The diagnosis was confirmed by skin biopsy.…

Schlagworte

Pityriasis lichenoides et varioliformis acuta Mucha Habermann immunosuppression specialized intensive care treatment silver toxicopathy Cyclosporine Ventilation Diagnosis Biopsy Blood After Klinische Pädiatrie