Pediatric treatment strategies of Pityriasis lichenoides et varioliformis acuta Mucha Habermann–effects and side effects
PP Wolf, M Sticherling, CJ Voskens, M Schroth · Klinische Pädiatrie · 2011 · Heft 03
Bibliografische Angaben
Zusammenfassung
Aims: Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta Mucha Habermann is a potentially lethal autoimmune disorder characterized by polymorphous generalized skin lesions that rapidely deteriorate associated with a severe disease pattern. Case report: We report on a 22 months old boy, to our knowledge the youngest out of 42 cases reviewed in the literature since its first description in 1966. He presented with bug-bite-like lesions that rapidely progressed into erythematous ulcers with hemorrhagic crusts and necroses including most of the integument. The diagnosis was confirmed by skin biopsy.…