Ectopic adrenal tissue next to the epididymis in a male newborn with congenital adrenal hyperplasia

Purpose/Background: Congenital adrenal hyperplasia (CAH) is an inherited defect of one enzyme responsible for the biosynthesis of cortisol, mostly 21-hydroxylase deficiency. Consequently, precursors in the enzymatic pathway accumulate, usually 17-hydroxyprogesterone (17-OHP) is elevated. There is a wide spectrum of phenotypes, classical CAH manifests in early life either with the severe salt-wasting form or with the virilizing form. In male patients occurance of intratesticular ectopic adrenal tissue, also called testicular adrenal rest tumor (TART), has been reported using ultrasound (1). Pediatric surgeons rep…