Primitive Neuroectodermal Tumor of the Pancreas An Extremely Rare Tumor
G. Bülchmann, T. Schuster, R. J. Haas, I. Joppich · Klinische Pädiatrie · 2000 · Heft 04 · S. 185-188
Bibliografische Angaben
Zusammenfassung
Abstract: Peripheral primitive neuroectodermal tumor (PPNET) is a malignant neoplasm of the peripheral nervous system and soft tissues. Representing the fourth case published we herein report a PPNET arising in the pancreas of a six year old girl. She presented with severe anemia due to ulcerative tumor growth and hemorrhage into the duodenum. From the first biopsy pancreatoblastoma was considered as histological diagnosis. Therefore pancreato-duodenectomy was successfully performed. Immunhistochemically, the tumor cells were positive for cytokeratines and several neuronal markers. Due to focal membranous staini…