CareLit Fachartikel
Electrophysiological study in juvenile asymmetric segmental spinal muscular atrophy (Hirayama disease)
W Dietrich, F Erbguth, G Berger, R Gerlach, I Bär, B Schmid · Klinische Neurophysiologie · 2008 · Heft 04
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1046237
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2008
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Zusammenfassung
Hirayama disease (HD) is characterized by slowly progressive distal amyotrophy of upper limb, usually monolateral, occurring predominantly in young Asian men. The aetiology of HD is not well understood, various aetiologic factors have been suggested such as microcirculatory disturbances of spinal cord or transient cord compression during neck flexion as well as autoimmune, atopic, and genetic factors. We report on a 21-year-old man who developed a slowly progressive weakness and atrophy with cold paresis of his right hand and forearm within four years. Neurological examination revealed slight muscular atrophy of…
Schlagworte
Atrophy
Cervical Cord
Denervation
Anatomy
Blood
After
Klinische Neurophysiologie
