IgG4-related sclerosing cholangitis mimicking cholangiocarcinoma in 10 patients
C Agne, F Puls, T Weismüller, H Bektas, HH Kreipe, MP Manns, K Rifai · Zeitschrift für Gastroenterologie · 2011 · Heft 08
Bibliografische Angaben
Zusammenfassung
Background & aims: IgG4 related sclerosing cholangitis (IgG4-SC) is a recently recognized form of sclerosing cholangitis. It is frequently associated with IgG-4-related autoimmune pancreatitis (AIP). It may represent a manifestation of a multisystem fibroinflammatory disorder. Lymphoplasmacellular infiltrates rich in IgG4-positive cells and fibrotic bile duct strictures are characteristic features of this disease. IgG4-SC can be successfully treated with corticosteroids. Methods: A full text search of the database of the Department of Histopathology's for the term „klatskin tumor“ was performed. All cases withou…