CareLit Fachartikel

Orbital Compression Syndrome in Sickle Cell Crisis

E. B. Mueller, K. Niethammer, D. Rees, C. J. Partsch · Klinische Pädiatrie · 2009 · Heft 05 · S. 308-309

Dokument
1105137
CareLit-ID
Jahr
2009
Publikation
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Metadaten
DOI
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Bibliografische Angaben

Zeitschrift
Klinische Pädiatrie
Autor:innen
E. B. Mueller, K. Niethammer, D. Rees, C. J. Partsch
Ausgabe
Heft 05 / 2009
Jahrgang 221
Seiten
308-309
Erschienen: 2009-09-01 00:00:00
ISSN
0300-8630

Zusammenfassung

Abstract This article is about a 9-year-old boy with known homozygous sickle cell disease who developed unilateral exophthalmia and eyelid swelling during a sickle cell crisis. The symptoms were due to a vaso-occlusive event in the orbital bones, known as orbital compression syndrome, which is a rare complication of sickle cell disease.

Schlagworte

exophthalmia sickle cell disease orbital compression syndrome periorbital cellulitis Exophthalmus Sichelzellkrankheit orbitales Kompressionssyndrom Orbitalphlegmone Sickle Orbital Compression Syndrome Crisis Known Disease Abstract