Acute liver failure in Hungarian Wilson disease patients
D Németh, A Folhoffer, E Horváth, J Schuller, P Tamási, L Kóbori, J Fazakas, B Nemes, Z Gerlei, D Görög, I Fehérvári, R Langer, M Szathmári, F Szalay · Zeitschrift für Gastroenterologie · 2013 · Heft 05
Bibliografische Angaben
Zusammenfassung
Background and Aims: Acute liver failure (ALF) is a rare form of Wilson disease (WD) developing mostly in young female patients. Use of chelating agents and supportive therapies including MARS (Molecular Adsorbent Recirculating System) in time may result in a remission in some cases making liver transplantation unnecessary. Patients and Methods: We analyzed data of 205 Wilson patients registered in the database of the 1st Department of Internal Medicine of Semmelweis University. We studied retrospectively the clinical data of 24 patients with acute liver failure. The diagnosis of WD was based on the internationa…