Diagnosis and managment of membranous Budd-Chiari syndrome
S Ciesek, MJ Bahr, B Boozari, J Lotz, H Wedemeyer, MP Manns, M Gebel · Ultraschall in der Medizin - European Journal of Ultrasound · 2008 · Heft 10
Bibliografische Angaben
Zusammenfassung
Budd-Chiari syndrome (BCS) is a rare disorder characterized by (non)thrombotic obstruction to hepatic venous outflow. Membranous obstruction of the inferior vena cava is a curable cause of a primary BCS and common in Asian countries. In contrast, membranous BCS is very rare in Western Europe or North America and so far, there is only very limited information on membranous BCS in the western world. We here report diagnosis and management of five Caucasian patients with membranous BCS. Out of 23 patients with BCS diagnosed between 2004 and 2007 we identify 5 with a membranous web of the IVC. None had a history of…
