Amyloidosis in our region – Apropos of a rare intestinal manifestation case
L Vén, K Czirják, M Francz, F Rácz, J Szegedi · Zeitschrift für Gastroenterologie · 2009 · Heft 05
Bibliografische Angaben
Zusammenfassung
Introduction: Amyloidosis is a disease caused by the extracellular deposition of autologous proteins with irregular structure. Classification is based on the precursor and produced amyloid proteins, whereas clinically systemic and local forms of the disease are known. Within the systemic form, the gastrointestinal system is affected in 60% of the secondary reactive AA cases and 1–8% of the primary AL cases. No reliable epidemiological data are available on the disease; its prevalence is estimated to be 5–12 patients per 1 million inhabitants per year in the western population with a characteristic dominance of m…