Bernard-Soulier Syndrome from the Perspective of the Obstetrician: A Case Report with a Review of the Literature
Erdinç Sarıdoğan, Taylan Onat, Senem Arda Düz, Görkem Tuncay, Nuray Abdurahmanova, Lumayat Orujova, Abdullah Karaer · Zeitschrift für Geburtshilfe und Neonatologie · 2023 · Heft 03 · S. 168-178
Bibliografische Angaben
Zusammenfassung
Abstract Objective Bernard-Soulier syndrome (BSS) is one of the rare inherited platelet disorders that is characterized by macrothrombocytopenia and adhesion abnormality due to the absence or malfunctioning of the membrane GPIb-IX-V complex. There is no high-quality evidence on obstetric management of BSS owing to its rarity. Here we report an uncomplicated delivery of an adolescent with BSS and review the literature on the topic of BSS and pregnancy. Methods PUBMED, EMBASE, COCHRANE, and Google Scholar databases were searched up to April 2022 without language and year restriction using the terms “Bernard Soulie…
