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The frequency of neuromyotonia in 37 patients previous diagnosed as benign cramp-fasciculation syndrome

S Wenninger, B Schoser · Klinische Neurophysiologie · 2014 · Heft 03

Dokument
873013
CareLit-ID
Jahr
2014
Publikation
PDF
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Metadaten
DOI
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Zeitschrift
Klinische Neurophysiologie
Autor:innen
S Wenninger, B Schoser
Ausgabe
Heft 03 / 2014
Seiten
–
Erschienen: 2014-03-12 00:00:00
ISSN
1434-0275

Zusammenfassung

Introduction: Neuromyotonia (NM), Isaacs-Zschoke-Mertens syndrome or continuous muscle fiber activity (CMFA), is a rare condition associated to complexes VGKC-antibodies. Clinically, fasciculations, myokymias, muscle stiffness and a myotonic appearance of movements after contraction are typical findings. Rarely, bulbar muscles can be involved, mainly seen as twitching of the tongue, swallowing or speaking problems. Major differential diagnosis is the benign cramp-fasciculation syndrome (BFS), which can also be seen either in healthy people or as motorneuron pre-syndrome. In electromyography, spontaneous irregula…

Schlagworte

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