Marfan syndrome – the early diagnosis and management
T Cuzor · Ultraschall in der Medizin - European Journal of Ultrasound · 2008 · Heft 05
Bibliografische Angaben
Zusammenfassung
Introduction: Marfan syndrome (MFS) is the inherited disorder of connective tissue that affects the cardiovascular system, eyes, skeleton; 26% of cases haven't any family history. Risk factors for aortic dissection (AD) in MFS include: aortic (Ao) diameter >50mm, Ao dilatation extending beyond the sinus of Valsalva, rapid rate of Ao dilatation (>5% per year, or 2mm/year in adults), and family history of AD. Objective: To identify the early predictors of cardiovascular complications in MFS patients. Material and methods: During a six year period, 84 patients were examined with aortic disorders (42 with AD, 42 wit…