Foix-Chavany-Marie Syndrome – Diplegia of the Craniopharyngeal Muscles with Dissociation between Voluntary and Automatic Movements

Introduction: Foix-Chavany-Marie syndrome (FCMS) presents clinically with anarthria, dysphagia and paralysis of the craniopharyngeal muscles with automatic voluntary dissociation. The classical and common form is a bilateral opercular lesion, in most cases associated with strokes. Rare causes are viral encephalitis, neurodegenerative diseases, congenital dysplasias and epilepsy. Case Report: We report the case of a 50-year-old female with two cardioembolic brain infarctions despite an anticoagulation therapy after replacement of the aortic valve in 1987. Three years ago she developed an incomplete bilateral infa…