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Gardner syndrome: The role of imaging methods

G Székely, Á Szilvás, K Vajda, J Farkas, A Kovács · Zeitschrift für Gastroenterologie · 2009 · Heft 05

Dokument
969045
CareLit-ID
Jahr
2009
Publikation
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Metadaten
DOI
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Bibliografische Angaben

Zeitschrift
Zeitschrift für Gastroenterologie
Autor:innen
G Székely, Á Szilvás, K Vajda, J Farkas, A Kovács
Ausgabe
Heft 05 / 2009
Seiten
–
Erschienen: 2009-05-07 00:00:00
ISSN
0044-2771

Zusammenfassung

Background: Gardner syndrome is a variant form of the classical, well known adenomatosus polyposis (FAP). Many different organs have noncancerous tissue masses including sebaceous cysts, epidermoid cysts, fibromas, desmoid tumors and osteomas. Petients with Gardner syndrome face a higher risk of developing colorectal cancer or other malignant conditions. The APC gene is linked to Gardner syndrome which stands for adenomatosus polyposis coli. A mutation of this gene provides an increased lifetime risk of developing polyps and cancer. The risk of developing colon cancer reaches almost 100%, other cancer risk move…

Schlagworte

Zeitschrift für Gastroenterologie